1、webzip 030 offline browser (unregistered) on 09/13/07 10:15:08.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0504.htmtitle: powerpoint presentation size: 3145 last modified: thu, 15 jun 2006 02:07:46 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:0

2、8.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0505.htmtitle: powerpoint presentation size: 6165 last modified: thu, 15 jun 2006 02:07:48 gmt本節(jié)應(yīng)了解、熟悉和掌握的知識(shí)點(diǎn)了解顱腦先天發(fā)育異常的分類 熟悉常見(jiàn)顱腦發(fā)育異常的影像學(xué)表現(xiàn) 神經(jīng)皮膚綜合征的影像學(xué)表現(xiàn)webzip 030 offline browser (unregistered) on 09/13/07 10:15:08.address

3、: 33/jpk/contents/g/yxx/doc/2-9.files/slide0506.htmtitle: powerpoint presentation size: 5554 last modified: thu, 15 jun 2006 02:07:48 gmt本節(jié)學(xué)習(xí)中的難點(diǎn)腦先天性發(fā)育異常的分類和影像學(xué)表現(xiàn) webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/

4、doc/2-9.files/slide0519.htmtitle: powerpoint presentation size: 3628 last modified: thu, 15 jun 2006 02:07:58 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0508.htmtitle: powerpoint presentation size: 2851

5、 last modified: thu, 15 jun 2006 02:07:48 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0509.htmtitle: powerpoint presentation size: 4811 last modified: thu, 15 jun 2006 02:07:48 gmt顱縫提早骨化、閉合，致頭顱畸形，包括舟狀 頭畸

6、形、短頭畸形、尖頭畸形、偏頭畸形、小 頭畸形等webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0510.htmtitle: powerpoint presentation size: 5317 last modified: thu, 15 jun 2006 02:07:50 gmt矢狀縫及頂顳縫提早閉合，頭顱左右徑生長(zhǎng)受限，前后徑生長(zhǎng)顯著 舟狀頭變形webzip 7.0

7、.3.1030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0514.htmtitle: powerpoint presentation size: 5582 last modified: thu, 15 jun 2006 02:07:56 gmt 顱底陷入枕骨大孔周?chē)琴|(zhì)，枕骨基底部、髁部、鱗部向顱腔內(nèi)陷入 扁平顱底前、中、后顱窩失去正常的階梯狀關(guān)系webzip 030 offline

8、 browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0515.htmtitle: powerpoint presentation size: 9979 last modified: thu, 15 jun 2006 02:07:56 gmt chamberlain：硬腭后緣與枕骨大孔后緣連線， 齒狀突高于此線3mm為異常 mcgregor： 硬腭后緣與枕骨最低點(diǎn)連線， 齒狀突高于此線6mm為異常webzip

9、030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0518.htmtitle: powerpoint presentation size: 2855 last modified: thu, 15 jun 2006 02:07:58 gmt 先天性腦積水：又稱積水性無(wú)腦畸形 病因：病因不明，可能與胚胎期頸內(nèi)動(dòng)脈發(fā)育 不良、母體感染、放射損傷有關(guān) 臨床與病理：頭顱迅速增大、面部比例失調(diào)， 智力低下，多在

10、一歲內(nèi)死亡 x線平片：頭顱呈球形增大，囟門(mén)大、顱縫寬、顱壁薄，顱面骨比例失調(diào) ct表現(xiàn)：額、頂、顳葉腦實(shí)質(zhì)幾乎消失，部分枕葉、基底神經(jīng)核、丘腦保存，小腦、腦干、四腦室一般正常 mri表現(xiàn)：幕上為水樣信號(hào)，大腦鐮、基底節(jié)、小腦及腦干結(jié)構(gòu)正常webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0533.htmtitle: powerpoint presentation size

11、: 6666 last modified: thu, 15 jun 2006 02:08:08 gmt 又稱 丹-瓦氏畸形 dandy-walker malformation 小腦半球及蚓部發(fā)育不良、四腦室中孔和側(cè)孔閉 鎖致四腦室擴(kuò)張和梗阻性腦積水webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0535.htmtitle: powerpoint presentation

12、 size: 6644 last modified: thu, 15 jun 2006 02:08:10 gmt后顱凹擴(kuò)大；巨大囊腫；小腦下蚓缺如，上蚓移位；小腦半球發(fā)育不良；腦干受壓，幕上腦積水鑒別：蛛網(wǎng)膜囊腫、大枕大池webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0536.htmtitle: powerpoint presentation size: 4915 l

13、ast modified: thu, 15 jun 2006 02:08:10 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0538.htmtitle: powerpoint presentation size: 8529 last modified: thu, 15 jun 2006 02:08:12 gmt 概述：前腦無(wú)裂畸形、無(wú)腦回、多小腦回、灰質(zhì)異 位

14、、腦裂畸形及腦溝回移位等，胚胎26月 病因不明：血管性，感染性，化學(xué)性webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0539.htmtitle: powerpoint presentation size: 9369 last modified: thu, 15 jun 2006 02:08:12 gmt 無(wú)腦回畸形：多見(jiàn)頂枕葉 ct、mr表現(xiàn): 腦表面光滑，腦回、溝缺

15、如 腦室擴(kuò)大, 側(cè)裂池、蛛網(wǎng)膜 下腔增寬webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0541.htmtitle: powerpoint presentation size: 4412 last modified: thu, 15 jun 2006 02:08:12 gmtwebzip 030 offline browser (unregistered)

16、 on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0551.htmtitle: powerpoint presentation size: 9206 last modified: thu, 15 jun 2006 02:08:20 gmt 病理： 融合型、非融合型 臨床：難治性癲癇，運(yùn)動(dòng)障礙，智力低下，發(fā) 育遲緩 影像學(xué)表現(xiàn)： 中央前、后回附近表面延伸至室管膜下 裂隙（p-e縫） 周?chē)べ|(zhì)不規(guī)則增厚webzip 030 offline browser

17、(unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0555.htmtitle: powerpoint presentation size: 4677 last modified: thu, 15 jun 2006 02:08:22 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jp

18、k/contents/g/yxx/doc/2-9.files/slide0558.htmtitle: powerpoint presentation size: 9096 last modified: thu, 15 jun 2006 02:08:24 gmt 病因：不清，可能與染色體異常及基因突變有關(guān) 病理：無(wú)腦葉、半腦葉、單腦葉型 影像學(xué)表現(xiàn)： 無(wú)腦葉 單腦室，少量腦組織，無(wú)中線結(jié)構(gòu)并發(fā) 顱面畸形 半腦葉 三腦室中線結(jié)構(gòu)缺如，或有較小大腦鐮， 縱裂淺 單腦葉 透明隔缺如，半球間裂淺webzip 030 offline browser (unregistered) on 09/

19、13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0560.htmtitle: powerpoint presentation size: 4410 last modified: thu, 15 jun 2006 02:08:26 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/

20、2-9.files/slide0561.htmtitle: powerpoint presentation size: 5290 last modified: thu, 15 jun 2006 02:08:26 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0562.htmtitle: powerpoint presentation size: 3840 las

21、t modified: thu, 15 jun 2006 02:08:28 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0521.htmtitle: powerpoint presentation size: 10453 last modified: thu, 15 jun 2006 02:07:58 gmt顱內(nèi)結(jié)構(gòu)經(jīng)顱骨缺損疝出顱外病理 顯性顱裂畸形型 腦膜

22、膨出型 腦膜腦膨出 型 腦室膨出型 囊性腦膜腦膨出臨床顱蓋組 膨出軟組織腫塊顱底組 眶、鼻、咽腫塊webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0522.htmtitle: powerpoint presentation size: 5654 last modified: thu, 15 jun 2006 02:08:00 gmtct：顱骨缺損，腦脊液密度膨出疝囊；軟

23、組織密 度疝囊mr：腦脊液信號(hào)膨出物、腦實(shí)質(zhì)信號(hào)膨出物，顱 內(nèi)腦室牽拉、變形、擴(kuò)張webzip 030 offline browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0526.htmtitle: powerpoint presentation size: 4407 last modified: thu, 15 jun 2006 02:08:04 gmtwebzip 030 offline b

24、rowser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0527.htmtitle: powerpoint presentation size: 9793 last modified: thu, 15 jun 2006 02:08:04 gmt 病因：先天性，后天性 病理：胚胎早期損傷嚴(yán)重，致完全缺如；胎晚期損 傷輕，致部分缺如 臨床：無(wú)癥狀，輕者視覺(jué)、交叉觸覺(jué)障礙，重者智 力低下、癲癇webzip 030 offl

25、ine browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0528.htmtitle: powerpoint presentation size: 9292 last modified: thu, 15 jun 2006 02:08:06 gmt部分缺如：壓部常見(jiàn)，壓部帶狀結(jié)構(gòu)消失，體變薄、 中斷完全缺如：側(cè)腦室擴(kuò)大、分離，前角小、后角大，三腦室上升，介側(cè)腦室間，頂緊鄰縱裂 池webzip 030 offli

26、ne browser (unregistered) on 09/13/07 10:15:09.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0529.htmtitle: powerpoint presentation size: 4678 last modified: thu, 15 jun 2006 02:08:06 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: http:/202.11

27、3.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0569.htmtitle: powerpoint presentation size: 9096 last modified: thu, 15 jun 2006 02:08:34 gmt 腦脊液在腦外異常的局限性積聚 病因 ：先天性 先天發(fā)育 后天性 外傷、感染、手術(shù)等 病理： 蛛網(wǎng)膜內(nèi)囊腫，多不與蛛網(wǎng)膜下腔部交通 蛛網(wǎng)膜下囊腫，多與蛛網(wǎng)膜下腔部相通 相鄰顱骨及腦組織呈受壓改變 臨床： 部分無(wú)癥狀，部分有輕癱、癲癇發(fā)作等webzip 030 offline browser (unreg

28、istered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0570.htmtitle: powerpoint presentation size: 8311 last modified: thu, 15 jun 2006 02:08:34 gmt 影像表現(xiàn)：ct、mri 邊緣光滑、腦脊液密度/信號(hào)區(qū)，無(wú)強(qiáng)化， 占位輕，顱骨變薄 位 置 外側(cè)裂池、大腦凸面、枕大池多見(jiàn) 鑒別診斷：膽脂瘤，大枕大池，腦穿通畸形囊腫webzip 030 offline

29、 browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0574.htmtitle: powerpoint presentation size: 5420 last modified: thu, 15 jun 2006 02:08:38 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: http:/202.113.

30、53.133/jpk/contents/g/yxx/doc/2-9.files/slide0578.htmtitle: powerpoint presentation size: 3580 last modified: thu, 15 jun 2006 02:08:42 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0580.htmtitle: powerpoi

31、nt presentation size: 6509 last modified: thu, 15 jun 2006 02:08:42 gmt一組遺傳性斑痣性錯(cuò)構(gòu)瘤病分兩型：神經(jīng)纖維瘤病型（神經(jīng)纖維瘤病型（webzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0584.htmtitle: powerpoint presentation size: 9235 last modi

32、fied: thu, 15 jun 2006 02:08:46 gmt nf-1型 nf-2型 cns病變 顱內(nèi)神經(jīng)腫瘤膠質(zhì)瘤 單、多發(fā)腦脊膜瘤叢狀神經(jīng)纖維瘤 脊神經(jīng)多發(fā)神經(jīng)鞘瘤其它 髓內(nèi)室管膜瘤、星形細(xì)胞瘤webzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0589.htmtitle: powerpoint presentation size: 4676 last mod

33、ified: thu, 15 jun 2006 02:08:48 gmtwebzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0590.htmtitle: powerpoint presentation size: 9739 last modified: thu, 15 jun 2006 02:08:50 gmt 病因：常染色體顯性遺傳，外顯率高 臨床：皮脂腺瘤、癲癇、智力低下webzip 030 offline browser (unregistered) on 09/13/07 10:15:10.address: 33/jpk/contents/g/yxx/doc/2-9.files/slide0591.htmtitle: powerpoint presenta